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KMID : 0387820090160010054
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Clinical Pediatric Hematology-Oncology
2009 Volume.16 No. 1 p.54 ~ p.58
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Effective Management of Kaposiform Hemangioendotheliomas Associated with Kasabach-Merritt Syndrome Using Chemotherapy
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Kim Myung-Joon
Jin Ji-Hoon
Lee Ji-Eun
Cheong Woo-Sik
Choi Gwang-Seong
Kim Joon-Mi
Kim Soon-Ki
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Abstract
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Although Kaposiform hemangioendothelioma (KHE) is a rare benign tumor, it is well known for its aggressiveness, showing mortality rates as high as 24% when progressed to Kasabach- Meritt syndrome. There are various therapies for KHE, such as oral prednisolone, intravenous methylprednisolone, interferon-α, surgical resection, chemotherapy and radiotherapy. We report a case of Kasabach-Meritt syndrome, which showed no response to oral prednisolone, intravenous methylprednisolone nor interferon-α, but a successful response to chemotherapy.
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KEYWORD
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Kaposiform hemangioendothelioma, Kasabach-Meritt syndrome, Chemotherapy
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